Purpose
Non-compaction of the ventricular myocardium is a rare disorder of myocardial morphogenesis usually diagnosed in pediatric age.
The diagnosis was echocardiographically made on the basis of a reported spongeous/compacted ratio >2 in one or more segments of the left ventricle during the diastolic period.We aimed toanalyze cardiac magnetic resonance imaging (CMR) characteristics in patients with left and right ventricular (LV,
RV) non compaction and assess its value in the diagnosis of it.
Fig. 1
Methods and Materials
We collected a consecutive series of 23 patients with a mean age of 19years.
Fig. 2
In all cases the diagnosis was performed by echocardiography.
Fig. 3, Fig. 4
We prospectively included patients drawn from groups given a potential differential diagnosis for Ventricular Non-compaction (VNC).
Fig. 5
We aimed to test the diagnostic accuracy of contrast enhancement CMR imaging in distinguishing pathological left/or both ventricular non-compaction and potential arrhythmic areas of spongy muscles.
Fig. 6
In all patients cardiac-gated T1 and T2 black-blood FSE images...
Results
In 12 cases we demonstrated by echocardiography an involvement of the ventricular apex.
In 8 cases the structural alterations involved also lateral wall of left ventricle.
CMR evaluation showed: ventricular apex involved in 15 cases,
lateral wall in 10 and all segments in 8cases.
In 7 cases we redetected the areas of the left ventrical wall dyskinesia,
the EPS confirmed at 6 of them the arrhythmic areas.
In 2 cases,
non-compacted myocardium was detected but echocardiography did not reach the N/C ratio> 2 as required...
Conclusion
Extent of non-compaction could be visualized correctly by MRI.
MRI with contrast enhancement in concordance with Doppler tissue ECG considered as the method of choice to detect NCVM and to establish functional and morphological myocardial changements of LV and RV.
Fig. 13
References
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Bakoulev Scientific Center for Cardiovascular Surgery of the Russian Academy of Medical Sciences