Moyamoya disease, CT angiography and digital subtraction angiography.

This poster is published under an open license. Please read the disclaimer for further details.

Congress:

ECR 2014

Poster Number:

C-1646

Type:

Educational Exhibit

Keywords:

CT-Angiography, Catheter arteriography, Vascular, Neuroradiology brain, Diagnostic procedure, Embolism / Thrombosis, Ischaemia / Infarction

Authors:

E. Montaño Claure¹, L. Valoyes Guerrero², D. Rodriguez³, L. Aja Rodriguez¹, A. Muntané Sánchez⁴, P. Mora Montoya¹; ¹Barcelona/ES, ²L'Hospitalet de Llobregat/ES, ³El Vendrell/ES, ⁴Hospitalet de Llobregat /ES

DOI:

10.1594/ecr2014/C-1646

DOI-Link:

https://dx.doi.org/10.1594/ecr2014/C-1646

Fig. 1: A: Rigth carotid angiography shows mild stenosis at the terminal part of the...

Fig. 2: AngioCT with coronal (A, B), axial (C) and sagittal (D) MIP reformat show...

Fig. 3: A: Rigth internal carotid artery angiography shows mild stenosis at the...

Fig. 4: A: Left internal carotid artery angiography shows stenoocclusive changes of...

Learning objectives

To describe CT angiography (CTA) and digital subtraction angiography (DSA) findings in moyamoya disease.

Background

The moyamoya disease is a rare cerebrovascular occlusive disorder of unknown origin. It is divided into two types according to whether this onset occurs in childhood or adulthood. It is characterized by bilateral progressive occlusion of the intracerebral vessels, initially affecting the terminal parts of the internal carotid arteries and pro-gressing to involve the anterior, middle and, in some cases, the posterior cerebral arteries. Simultaneously, a dense network of abnormal collateral vessels is formed at the base of the brain angiographically resembling a puff of...

Findings and procedure details

The main features of moyamoya disease are bilateral stenosis of the internal carotid bifurcations and basal telangiectasias comprising dilated collateral lenticulostriate and thalamoperforating arteries. Initial symptoms are due to either cerebral ischemia or intracranial hemorrhage. The hemorrhage may be subarachnoid, intraparenchymal, or intraventricular and is sometimes associated with a saccular aneurysm (usually in the vertebrobasilar system). In children the initial symptoms are usually due to ischemia whereas adults often have hemorrhagic manifestations. Collateral circulation forms from a number of sources: via the abnormal moyamoya vessels...

Conclusion

CTA is useful in the diagnosis and classification of moyamoya disease. CTA findings of moyamoya could be well correlated with DSA findings.

Personal information

E. Montaño Claure, Department of Radiology, Hospital Universitari de Bellvitge, Feixa Llarga, sn 08907 Hospitalet de Llobregat, Barcelona L. Valoyes Guerrero, Department of Radiology, Hospital Universitari de Bellvitge, Feixa Llarga, sn 08907 Hospitalet de Llobregat, Barcelona D. Rodriguez Bejarano, Department of Radiology, Hospital Universitari de Bellvitge, Feixa Llarga, sn 08907 Hospitalet de Llobregat, Barcelona L. Aja Rodriguez, Department of Radiology, Hospital Universitari de Bellvitge, Feixa Llarga, sn 08907 Hospitalet de Llobregat, Barcelona A. Muntané Sánchez, Department of Radiology, Hospital Universitari de Bellvitge, Feixa Llarga, sn...

References

[1] Suzuki J, Kodama N. Moyamoya disease: a review. Stroke 1983; 14:104-114. [2] Mujikura S, Takahashi S, Higano S, et al. The Relationship between Cerebral Infarction and Angiographic Characteristics in Childhood Moyamoya Disease. AJNR Am J Neuroradiol 1999; 20:336-343. [3] Togao O, Mihara F, Yoshiura T, et al. Cerebral Hemodynamics in Moyamoya Disease: Correlation between Perfusion- Weighted MR Imaging and Cerebral Angiography. AJNR Am J Neuroradiol 2006; 27:391-397. [4] Yoon H, Shin H, Lee M et al. MR Angiography of Moyamoya Disease Before and After...