1. To review the classification, clinical manifestations and imaging features of fibromatosis. 2. To illustrate the imaging findings with pathologic correlation.

The musculoskeletal fibromatosis comprise a wide range of lesions with a common histopathologic appearance. The can be divided into two major groups: superficial and deep. The superficial fibromatosis are typically small, slow- growing lesions and include palmar fibromatosis, plantar fibromatisis, juvenile aponeurotic fibroma, and infantile digital fibroma. The deep fibromatosis are commonly large, may grow rapidly, and are more aggressive. They include infantile myofibromatosis, fibromatosis colli, extra-abdominal desmoid tumo, and aggressive infantile fibromatosis. Advanced imaging (ultrasonography, computed tomography, and magnetic resonance imaging) demonstrates lesion extent....

INTRODUTION Fibromatosis is a rare mesenchymal tumor characterized histologically by proliferation of fibroblasts and myofibroblasts with marked production of intercellular collagen. It comprises a broad group of fibrous tissue proliferations of similar histologic appearance that has biologic behavior intermediate between that of benign fibrous lesions and fibrosarcoma. Fibromatosis was first described more than 150 years ago by McFarlane. Because of its rarity, most published series describe only small numbers of patients. The incidence is estimated to be between three or four cases per million per...

Fibromatoses comprise a large spectrum of lesions and radiologists play an important role in the diagnsosis and may help guide the often difficult therapy and management of these lesions. We hope that the information provided in this exhibit will be useful for the readers.

AUTHORS ADONIS MANZELLA, MD,MSc MARIANA VASCONCELOS, MD STERFFERSON MORAIS, MD DIEGO SOUZA, MD ERICK CAVALCANTE, MD MILENA ALMEIDA, MD CRISTINE ZELAQUETT DE SOUZA, MD EOLO ALBUQUERQUE, MD MARCELO SOUZA, MD

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