Learning objectives
-To recognize typical and atypical pulmonary image findings of scleroderma and pneumoconiosis.
- To be aware of the possibility of having scleroderma and synchronic pneumoconiosis in the same patient and avoid “satisfaction of search” error.
Background
Progressive systemic sclerosis or scleroderma is a generalized disease of the connective tissue in which up to 75% of the cases evidence pulmonary affection.
This disease is commonly associated with usual interstitial pneumonia,
non-specific interstitial pneumonia,
pulmonary vasculitis,
and pulmonary hypertension; nevertheless it can also be found associated with other lung diseases without a direct physiopathological relation.
This is the case of pulmonary manifestations of scleroderma and synchronic inhalation lung disease.
Pneumoconiosisis a broad group of lung diseases that result from the inhalation of dust...
Findings and procedure details
1- HRCT findings of progressive systemic sclerosis
HRCT findings of interstitial fibrosis in progressive systemic sclerosis are similar to those of idiopathic pulmonary fibrosis (IPF),
including ground-glass opacity,
consolidation,
fine reticular opacities,
coarse or irregular reticulation,
traction bronchiectasis and honeycombing.
Abnormalities typically show a subpleural and lower lobe predominance and often involve the lung periphery in a concentric fashion (Fig.
1).
As with the other collagen diseases,
there is a tendency for scleroderma to show a finger reticular pattern that is typical of IPF,
and...
Conclusion
Seventyfive percent of patients with scleroderma have lung involvement in their chest HRCT,
even without respiratory symptoms; most cases show some degree of interstitial fibrosis.
.
Other chest HRCT features may suggest synchronic illness and change management and prognostic.
References
- W.
Richard Webb,
Nestor L.
Müller,
David P.
Naidich.
Alta resolución en TC de Pulmón.
3ª edición.
Philadelphia: Marban; 2003.
-W.
Richard Webb,
Charles B.
Higgins.
Thoracic imaging.
Pulmonary and Cardiovascular Radiology.
USA; Lippincott Williams and Wilkins,
2005.
- J.
A.
Verschakelen,
W.
De Wever.
Computed Tomography of the Lung.
Belgium: Springer; 2007.