Learning objectives
The aim of this work is to focus on the median arcuate ligament syndrome also known as Dunbar Syndrome,
a rare cause of abdominal pain,
and to show the main radiological findings (characteristics on imaging) of this pathology.
Background
Dunbar syndrome,
or median arcuate ligament syndrome (MALS),
is a condition caused by an extrinsic compression of the celiac trunk,
and sometimes of the celiac plexus,
by the median arcuate ligament (MAL).
This is a fibrous band at the level of the Th12/L1 vertebral bodies,
across the aortic hiatus,
that connects the right and left diaphragmatic crura.
However,
the location of MAL is very variable.
In fact,
the celiac trunk,
in 33% of cases,
originates at the same level or above the MAL [1].
In...
Findings and procedure details
Imaging support is essential; diagnosis can be made through Duplex US and Angiography CT,
that permit to show a lower implant of the arcuate ligament and the narrowing of the origin of celiac artery with a characteristic hooked appearance.
A poststenotic dilatation and collateral vessels could be present in severe stenosis.
A fundamental characteristic of this condition is the aggravation of stenosis following respiratory movements; the stenosis determined by the MAL,
on the origin of the celiac trunk is more pronounced in expiration.[12]
Conclusion
Dunbar syndrome or MALS is a controversial condition and the debate of scientific community is still open.
The radiologist should have a good knowledge and awareness of this disease because he plays a key role: thanks to radiological findings and clinical aspects he can do a correct differential diagnosis and address patients in right management,
often curative.
References
1.
Ozdil Baskan MD*,
Emre Kaya,
MD,
Fatma Zeynep Gungoren,
MD,
Cengiz Erol,
MD.Compression of the Celiac Artery by the Median Arcuate Ligament: Multidetector Computed Tomography Findings and Characteristics.Canadian Association of Radiologists Journal 66 (2015) 272 e 276
2.
Jeffrey Kah Keng Fong,
Angeline Choo Choo Poh,
Andrew Gee Seng Tan,
Ranu Taneja.Imaging findings and clinical features of abdominal vascular compression syndromes.AJR:203,
July 2014
3.
Levin DC,
Baltaxe HA.
High incidence of celiac axis narrowing in asymptomatic individuals.AmJ Roentgenol Radium Ther Nucl Med1972;116:426–429
4.
Dunbar...