- Describe the characteristic radiological findings of Dyke-Davidoff-Masson syndrome, as well as its clinical presentation and diagnostic methods. - Illustrate this syndrome with images from 3 cases of our hospital.

Dyke-Davidoff-Masson syndrome (DDMS) is a rare entity that presents with atrophy/hemicerebral hypoplasia secondary to brain injury, usually in the fetal period or in early childhood, and is accompanied by ipsilateral compensatory bone hypertrophy and contralateral hemiparesis. There are two types of DDMS: congenital (infantile) and acquired (during early life due to brain damage, usually traumatic). Prenatal causes include congenital abnormalities, cerebral infarction, vascular malformations, infections, and gestational vascular occlusion, primarily involving the middle cerebral vascular territory. Birth trauma, hypoxia, intracranial hemorrhage, tumors, infections, and prolonged...

We review the cases diagnosed in our health area from 2012 to 2016: - Case 1:Infant of 8 months with left hemiparesis predominantly in the left arm. - Case 2: A 3-year-old girl (international adoption without prenatal or postnatal data) presenting partial motor epileptic crisis in the context of febrile symptoms. - Case 3: An 8-year-old boy with a clinic of paresthesias in hand and right jaw of two months of evolution. Imaging studies were performed in the 3 cases, both transfontanelar ultrasound in lactation...

- Dyke-Davidoff-Mason syndrome is a rare pediatric entity, secondary toimpaired cerebral perfusion. It presents characteristic radiological findings, expressed by cerebral hemiatrophy associated with compensatory bone changes, represented in our cases. Clinically it manifests with focal neurologic signs. - The diagnosis is made by CT and MRI, and as radiologists, we must know these typical findings to make the definitive diagnosis. MRI is a valuable method of examination in the analysis of cerebral hemiatrophy as it has the ability to detect changes in the cerebral hemispheres...

- BeheraMR, PatnaikS and MohantyAK. Dyke-Dabisson-Masson Syndrome. J Neurosci Rural Pract. 2012 Sep-Dec; 3(3): 411–413. - Pareshkumar A. Thakkar and Reema Haresh Dave.Dyke–Davidoff–Masson syndrome: A rare cause of cerebral hemiatrophy in children. J Pediatr Neurosci. 2016;11(3):252–254.