Aims and objectives
Rhabdomyosarcoma is the most common mesenchymal malignancy of the child,
it develops in the orbit in 10% of cases and is more often displaced by rapidly evolving exophthalmia and / or swelling.
Imaging (ultrasound,
CT,
MRI) plays an important role in the positive diagnosis that is confirmed histologically.
By reporting a series of 13 children,
the aim of this work is to report the radiological aspects of these tumors and to show the interest of the imaging in the positive diagnosis,
the assessment of extension...
Methods and materials
We conducted a retrospective descriptive study of 13 case reports carried out between 2014 and 2017 in the Pediatric radiology and Child Surgery departments at the mother and child hospital at the University Hospital MOHAMED VI.
Results
The average age of our patients was 5 years,
mostly female (n = 7) .
The most frequent reason for consultation was unilateral exophthalmia in 92% of cases (Figure 1).
All our patients underwent a CT examination,
five of them only performed MRI; for financial reasons .
· CT findings:
CT scan shows a mass iso dense with respect to the muscles,
extra-connal,
homogeneous and well circumscribed,
taking the contrast in a moderate to intense way (figure 2),
aspect found in our series (figure 7),...
Conclusion
Orbital rhabdomyosarcoma is the most common primary orbital malignant tumor in children,
and its rapid diagnosis can save the life of the individual.
Advances in imaging,
including computed tomography and magnetic resonance imaging,
significant progress in chemotherapy and radiotherapy have made orbital rhabdomyosarcoma a pediatric cancer with a relatively good prognosis.
References
1.
Rao AA,
Naheedy JH,
Chen JY,
Robbins SL,
Ramkumar HL (2013) A clinical update and radiologic review of pediatric orbital and ocular tumors.
J Oncol 2013: 22 pages.
2.
Bonnin N,
Nezzar H,
Viennet A et al.,
“Case report of a 2-year-old child with palpebral rhabdomyosarcoma,”J Fr Ophtalmol2010; 33( 3): 178–84.