Learning objectives
To elucidate imaging features of Fibrous dysplasia on radiography ,CT,CECT,PET CT.
To discuss the Key Imaging features of FD with differential diagnosis.
Background
.Fibrous dysplasia is a congenital,
non-hereditary,
progressive,
skeletal disorder by which normal bone is replaced by a variable amount of structurally weak fibrous and osseous tissue.
It is characterized by the presence of woven bone.
The normal formation of bone would involve a process by which woven bone appears first and later matures into lamellar bone.
Under concentrated light,
lamellar bone trabeculae (rows of cells bridging an intercellular space) show widely spaced parallel birefringent lines,
rimmed with osteoblasts and osteoclasts.
In fibrous dysplasia,
where bone...
Imaging findings OR Procedure Details
The radiologic appearance of fibrous dysplasia can appear as a lucent area with a sclerotic rim.
In the skull base and facial bones,
fibrous dysplasia manifests as marked sclerosis and bone thickening.
Fibrous Dysplasia
Radiographic Features
Terms used to describe the internal
architecture include:
• ground glass
• orange peel
• cotton wool
• thumb whorl
The lesion may contain a central lucent area
that is analogous to a simple bone cyst
Conclusion
This Educational exhibit illustrates the typical and atypical Imaging features of fibrous dysplasia.
References
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Fibrous dysplasia: MR imaging characteristics with radiopathologic correlation.
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Campanacci M.
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Wien,
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Ozek C,
Gundogan H,
Bilkay U,
et al.
Craniomaxillofacial fibrous dysplasia.
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Yamaguchi T,
Dorfman HD,
Eisig...