To describe and illustrate the main tomographic findings of abdominal vascular syndromes in their different etiologies,
such as compressive and congenital.
When we contemplate the study of the vascular anomalies,
we can briefly separate these patologies in neoplastic,
compressive and congenital in nature.
In this current study,
we will give emphasis to the vascular anomalies that constitue notable clinical syndromes with abdominal impairment,
particularly those not of neoplastic nature.
The purpose of this study is to describe and ilustrate the main image findings regarding these syndromes which are of great value to medical knowledge.
Findings and procedure details
1 VASCULAR CONGENITAL SYNDROMES
1.1 RENDU-OSLER-WEBER SYNDROME
also known as hereditary hemorrhagic telangiectasia,
consists of a variable combination of capilary and arteriovenous malformations and yet arteriovenous fistulas (therefore,
of high flow),
of visceral and mucocutaneous distribution,
impairing preferably the brain,
lungs and gastrointestinal tract.
These patients usually present epistaxis around 10 years of age as a first manifestation of the disease and these episodes tend to worsen as time passes by.
It is believed that up to 60% of patients have hepatic...
Of the congenital vascular abdominal syndromes described above,
it can be noted a distinction between two sets of diseases according to the quality of blood flow in these vascular malformations,
which can be set as such: blue rubber bleb nevus and Klippel-Trénaunay syndrome,
with no arterial components and,
of low blood flow,
are composed of findings easily identified since birth,
of slow but constant progression with coagulation disturb as a main complication.
On the other hand,
with arterial high blood flow components,...
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