Type:
Educational Exhibit
Keywords:
Arteriovenous malformations, Education, MR, CT, Arteries / Aorta, Abdomen
Authors:
D. B. Montel1, D. M. Tridente2, I. P. Vilas Boas3, L. M. Fernandes 4, F. Lewin3, L. Saad3, G. Bittencourt Basso3; 1São Paulo, Sã/BR, 2Sao Paulo, SP/BR, 3São Paulo/BR, 4São paulo , São paulo /BR
DOI:
10.1594/ecr2018/C-0779
Conclusion
Of the congenital vascular abdominal syndromes described above,
it can be noted a distinction between two sets of diseases according to the quality of blood flow in these vascular malformations,
which can be set as such: blue rubber bleb nevus and Klippel-Trénaunay syndrome,
with no arterial components and,
therefore,
of low blood flow,
are composed of findings easily identified since birth,
of slow but constant progression with coagulation disturb as a main complication.
On the other hand,
Rendu-Osler-Weber syndrome,
with arterial high blood flow components,
manifests later in life as opposed to the previous diseases,
showing systemic complications that can lead to a higher morbidity.
The compression of abdominal vessels can be assymptomatic or result in clinical findings that vary from slight to severe.
Therefore,
their radiological findings should be interpreted accordingly to the clinical story and secondary hemodinamic repercussions.
The acknowledgement of compression syndromes and an attentive assessment of the vascular structures in the proper plains should be routine.
A high morbidity and mortality of the vascular syndromes make the radiologist essential in the management of these patients,
resulting in a better prognosis.
It is,
therefore imperative to master the knowledge of this set of diseases,
specially for the emergency radiologist.