To review Mid-Aortic syndrome (MAS) clinical aspects and its correlation with imaging features.
To illustrate key radiological findings of this syndrome.
Mid-Aortic syndrome (MAS) is a rare entity characterized by narrowing of the abdominal aorta and its major branches.
There will be involvement of the renal arteries in most patients.
Although stenosis of the thoracic aorta is possible,
it is uncommon.
Tipically affects children and young adults.
Most cases are idiopathic.
There are several theories about its possible origin being the most accepted a probable lack of fusion of both dorsal aortas in embryonic life with atrophy and stenosis of one of them.
MAS may also...
Findings and procedure details
Mid-Aortic syndrome (MAS) is characterized by stenosis of the abdominal aorta frequently associated with a concomitant stenosis of the renal and visceral arteries Fig.1.
Artery stenosis tipically involves the ostium of the vessel.
MAS is typical of childhood without a predilection for sex.
In most cases it is idiopathic.
Although there is no clear consensus on the mechanism by which it occurs,
a congenital anomaly has been suggested.
A lack of fusion of both dorsal aortas in embryonic life is the most accepted theory.
MAS is an important cause of hypertension in childhood and a rare but potentially lethal entity.
As most patients are children and young adults,
the clinical benefits of early diagnosis and treatment are undebatable.
Radiologists should understand the key radiologic findings and suspect this disease when it is present.
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Hamilton.Mid-aortic syndrome: long-term outcome of 36 children.
Idiopatic mid-aortic syndrome in children.
Reno-vascular hypertension in chilhood:...