The purpose of this presentation is to demonstrate the role of each imaging method,
such as ultrasonogrphy,
MRI and CT in diagnosis of desmoid tumors in pediatric patients.
Desmoid tumors are benign soft tissue tumors (known as aggressive fibromatosis) that arise from musculoaponevrotic structures.
It was first described in 1832 by McFarlane and it accounts for 0.03% of all neoplasms.
Desmoid tumors are rarely encountered in children,
but they are more aggressive at pediatric age.
These tumors often develop on postsurgical or posttraumatic scars and can also be related to pregnancy and oral contraceptive use.
It has been established the association with Gardner syndrome and familial adenomatous polyposis.
Desmoid tumors have a very...
Findings and procedure details
Ultrasonography and Elastography findings
aggressive fibromatosis appears as a homogeneos,
hypoechoic soft tissue mass.
It may show variable vascularity and can be lobulated.
When the tumor has large dimensions it may cause difficulty establishing the origin of the lesion.
4 and 5)
Elastography is not a common method of diagnosis for desmoid tumors because it is demonstrated that elastography have the same sensitivity as grey-scale US-scan.
On CT desmoids tumors appear as relatively homogeneos masses,
MRI is the most sensitive method of diagnosis for tumoral extension in adiacent structures because of its excellent soft tissue contrast .
The T2-weighted images may have prognostic value because of the T2 high signal associated with higher cellularity,
which means rapid growth.
Update on desmoids tumors,
Annals of Oncology 23: 562-569,
Diagnostic problems of abdominal desmoids tumors in various locations,
European Journal of Radiology 62:180-185,
Kotilingam D, Wei C, Ballo M.T,
Pisters P.T.W,Lazar A, Patel S.R,
Optimizing Treatment of Desmoid Tumors,
Journal of Clinical Oncology vol 25,