To illustrate Multidetector CT manifestations of a variety of congenital pulmonary vascular malformations.
To emphasize the role of multidetector CT angiography in diagnosis of pulmonary vascular anomalies.
Congenital anomalies of the thoracic vascular system are an important cause of morbidity and mortality in infants and children 1.
Congenital thoracic vascular anomalies occur in the thoracic aorta and branch arteries,
thoracic systemic veins,
and the pulmonary veins 2.
In this pictorial educational exhibit,
pulmonary vascular anomalies are focussed.
Congenital pulmonary vascular anomalies:
Pulmonary arterial anomalies
Pulmonary venous anomalies
Pulmonary arterial anomalies:
Congenital pulmonary arterial anomalies include hypoplasia,
pulmonary artery sling,
pulmonary artery aneurysm,
These anomalies most often...
Findings and procedure details
MDCT Procedure Details:
Computed Tomography has a vital role in diagnosing congenital vascular anomalies.
For CT pulmonary angiography (CTPA) and cardiac anomaly CT examinations,
scan is performed from lung apex till level of adrenals with a large field of view.
A 1.25-mm collimation should be used,
which can be reconstructed at 0.75- 1 mm intervals with a targeted field of view.
A pitch of 3 or 6 is required depending on the the patient's ability to hold their breath.
Average of 120 mL of nonionic...
MDCT with the use of multiplanar reconstruction enables highly accurate differentiation among pulmonary vascular abnormalities.
MDCT pulmonary angiography with multiplanar and three-dimensional techniques should be the method of choice for preoperative morphologic assessment of vascular diseases in adult and pediatric patients.
MDCT is an accurate method for the diagnosis of congenital anomalies involving both pulmonary arteries and veins and also for preoperative planning and post operative evaluation.
All authors are consultant radiologists at Rehman Medical Institute Peshawar.
Ummara Siddique Umer
FCPS (Radiology) ,EDiR (EBR)
Consultant Radiologist &Assistant Professor of Radiology
Rehman Medical Institute Peshawar
We would like to thank Mr.Rafeeq,
Arshad and Mr.
Junaid for their help in data collection.
1. El-Gaber NA,
Role of 16-multidetector CT angiography in assessment of arterial and venous pulmonary anomalies in pediatrics.
The Egyptian Journal of Radiology and Nuclear Medicine 2013;44:483-95.
2. Hellinger JC,
Congenital thoracic vascular anomalies: evaluation with state-of-the-art MR imaging and MDCT.
Radiol Clin N Am 2011;49:969–99.
3. Ziolkowska L,
Turska-Kmiec A .
Chromosome 22q11.2 microdeletion in children with conotruncal heart defects: frequency,
associated cardiovascular anomalies,
and outcome following cardiac surgery.
Eur J Pediatr 2008;167:1135–114.