Type:
Educational Exhibit
Keywords:
Not applicable, Congenital, Complications, MR, CT, Cardiac
Authors:
M. R. Bursupalle1, A. Ayyappan2, V. jineesh2, A. Alex2; 1TRIVANDRUM, Kerala/IN, 2TRIVANDRUM/IN
DOI:
10.26044/ecr2020/C-11065
Background
•
• Single ventricle(SV) heart is “Defined as entire AV junction is connected to only one chamber in the ventricular mass
• SV heart is a rare condition with estimated prevalence of 1:10000.
Different classifications of SV given in tables 1, 2 & 3
Pathophysiology
• Mixing of pulmonary and systemic circulation
• SV bears the burden of pumping blood to both systemic and pulmonary circulation
• Presence of either systemic or pulmonary outflow tract obstruction
• Atrial septal defect – open or restrictive(Restrictive defect may cause increase in CVP or LA pressure)
• AV valve regurgitation may cause ventricular failure
Clinical presentation
• Cyanosis – in pulmonary outflow tract obstruction
• Dyspnoea, lethargy and poor feeding- in systemic outflow tract obstruction
• Shock - severe aortic obstruction/arch hypoplasia/interruption of aorta due to closure of PDA with 1st week of neonatal life
• Heart failure - excess volume overload in large AVCD /AV valve regurgitation
Goal of surgical palliation in SV hearts
• To separate the systemic and pulmonary circuits- results normal or near normal oxygen saturation.
• To divert systemic venous return directly into the pulmonary vascular bed – to decrease the volume load on a functional single ventricle.