Left ventricular non-compacted cardiomyopathy (LVNC) is a rare disease.
It is morphologically characterized by increased left ventricular (LV) trabeculation and deep intertrabecular recesses communicating with the LV cavity.
The disease usually has genetic or inherited pattern.
But clinical manifestations and severity of clinical course often do not correlate with the severity of morphological changes.
It is well known that prominent LV trabeculations may be found in up to 20-30% of patients without LVNC (in athletes,
patients with LV overload due to valvular or congenital heart...
Methods and Materials
The poster presents 18 cases of children and teenagers (age range 7 months – 16 year old) with diagnosis of LVNC and LV hypetrabeculation of secondary origin.
Patients were examined with cardiac echocardiography and cardiac MRI (1.5 tesla scanner),
in 3 cases- with low-dose cardiac CT.
Diagnosis of LVNC was based on Petersen’s criteria and clinical manifestations of the disease.
Poster presents a spectrum of clinical cases with true LVNC and cases when hypertrabeculations have secondary or incidental origin,
being combined with other cardiac diseases.
Typical cases of LV non-compaction are shown on Fig.
These patients were asymptomatic but they had typical signs of LVNC by echocardiography and MRI.
One more patient with LVNC had died from fatal pulmonary thromboembolism (Fig.
A patient with a large atrial septal defect,
RV dilation and trabecular layer on top of the LV,
also had MR images,...
Typical cases of LVNC are easy diagnosed by echocardiography or MRI.
quite often different cardiac diseases (e.g.
CHD) accompanied with increased trabeculation of LV.
In order to avoid hyperdiagnosis of LVNC,
cardiac MRI is needed.
In asymptomatic patients with some minor areas of non-compacted myocardium or increased trabeculations usually there is no need for treatment,
but special care should be taken about cases with true LVNC.
On the large scale,
this demonstration of clinical cases with LVNC and LVNC-like manifestations of different...
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