Learning objectives
Objective of this study is to evaluate the meningoencephaloceles of the skull base,
define the classification,
the causes of the onset and the imaging characteristics.
Background
Meningoencephaloceles are a congenital or acquired malformation characterized by protrusion of the meninges and brain tissue through a defect of the skeleton of the skull.
CLASSIFICATION
According to their location are classified as: occipital,
sincipital (naso-frontal,
naso-ethmoidal,
nasal-orbital),
of the cranial vault,
of the posterior fossa and of the skull base.
Have an incidence of between 0.1 and 0.5 in every 1000 live births with no significant gender differences.
Has not been demonstrated familiarity.
MENINGOENCEPHALOCELES OF THE BASE
Meningoencephaloceles of the base of the skull...
Imaging findings OR Procedure details
TRANS-SPHENOIDAL MENINGOENCEPHALOCELES
The trans-sphenoidal variant is the most common among encephaloceles of the base with an annual incidence of about 1 in every 700,000 live births.
Pollock has proposed the following etiological theories to explain its occurrence: lack of fusion of the ossification centers,
increased intraventricular pressure with progressive erosion of the underlying bone or postnatal enlargement of small bony dehiscences,
persistence of the cranio-pharyngeal canal.
THE CRANIO-PHARINGEAL CHANNEL OR STERNBERG'S CHANNEL
The persistence of this channel is a rare entity described for the first...
Conclusion
Meningoencephaloceles of the skull base are very rare pathological entity.
Their recognition first makes use of the detection of the symptoms and then of CT scan and MRI also useful in post-operative evaluation.
References
Recurrent meningitis and persistence of craniopharyngeal canal: case report.Neurocirugía512009; 20.
Gigant TransethmoidalMeningoencephalocele Operated byFull Endonasal Endoscopic Approach: Case ReportHindawi Publishing CorporationCase Reports in MedicineVolume 2012,
Article ID 763259,
4 pagesdoi:10.1155/2012/763259
Encephalomeningocele cases over 10 years in Thailand: a case series
Sitthiporn Agthong*1 and Viroj Wiwanitkit -BMC Neurology 2002,
2:3
CSF Rhinorrhea and RecurrentMeningitis Caused byTransethmoidalMeningoencephaloceles.
Parul GargVinita RathiSatish K.
BhargavaAnju Aggarwal*.INDIAN PEDIATRICSVOLUME 42__OCTOBER 17,
2005
Bernhard Schick · Dominik Brors · Andreas PrescherSternberg’s canal – cause of congenital sphenoidal meningocele.Eur Arch Otorhinolaryngol (2000) 257 :430–432...
Personal Information
Pollice Saverio MD
Department of Radiology - Neuroradiology.
"L.
Bonomo" Hospital.
chief Tommaso Scarabino MD
Andria (postal code 76123) BT - Italy
mail:
[email protected] -
[email protected]