POSTER SECTIONS Coverpage Learning objectives Background Findings and procedure details Conclusion Personal information and conflict of interest References

ECR 2021 / C-10662

Congenital ear malformations: a practical overview.

Congress:

ECR 2021

Poster Number:

C-10662

Type:

Educational Exhibit

Keywords:

Ear / Nose / Throat, CT, Imaging sequences, Congenital

Authors:

M. Da Silva Torres, L. García Suárez, S. González Sánchez, �. Meilán Martínez, M. Martínez-Cachero García, P. Corujo Murga, L. M. Guadalupe González, S. A. Jarreta, F. García Arias; Oviedo/ES

DOI:

10.26044/ecr2021/C-10662

DOI-Link:

https://dx.doi.org/10.26044/ecr2021/C-10662

References

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D’Arco F, Sanverdi E, O'Brien WT, et al. The link between inner ear malformations and the rest of the body: what we know so far about genetic, imaging and histology. Neuroradiology 2020;62:539–44
Koral K. Embryology, anatomy, normal ﬁndings, and imaging techniques. In: Coley B, ed. Pediatric Diagnostic Imaging, 12th ed, Philadelphia: Elsevier Inc.; 2013:87–9.
Bartel-Friedrich S, Wulke C. Classification and diagnosis of ear malformations. GMS Curr Top Otorhinolaryngol Head Neck Surg. 2007;6:1865-1011.
Weerda H. Chirurgie der Ohrmuschel. Verletzungen, Defekte und Anomalien. Stuttgart: Thieme; 2004. S. 105-226.
Romo LV, Casselman JW, Robson CD. Temporal bone: congenital anomalies. In: Som PM, Curtin HD, eds. Head and neck imaging. 4th ed. Vol 2. St Louis, Mo: Mosby, 2003; 1119–1140.
Altmann F. Congenital aural atresia of the ear in men and animals. Ann Otol Rhinol Laryngol. 1955;64:824-58.
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Jackler RK, Luxfor WM, House WF. Congenital malformations of the inner ear: a classification based on embryogenesis. The Laryngoscope 2009; 97(S40): 2–14.
Sennaroğlu L, Bajin MD. Classification and current management of inner ear malformations. Balkan Medical Journal 2017; 34: 397–411.
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Quirk B, Youssef A, Ganau M, D'Arco F. Radiological diagnosis of the inner ear malformations in children with sensorineural hearing loss. Br J Open. 2019;1(1)
D'Arco F, Talenti G, Lakshmanan R, Stephenson K, Siddiqui A, Carney O. Do measurements of inner ear structures help in the diagnosis of inner ear malformations? A review of the literature. Otol Neurotol 2017; 38: e384–92.

Fig 1: Embryological development of the ear

Fig 2: Axial (A) and coronal (B) images of the normal anatomy of the EAC.

Fig 3: Ossicular chain anatomy.

Fig 4: Axial (A) and coronal (B) images of the middle ear.

Fig 5: Axial (A, B, and C) and oblique sagittal (D) images of the inner ear.

Fig 6: Different dysplasia grades of the auricle according to Weerda.

Fig 7: Bilateral fibrocartilaginous and bony EAC stenosis on axial (A) and coronal (B)...

Fig 8: Combined malformations of external and middle ear according to Altmann.

Fig 9: 8. Left congenital aural atresia (third degree). The left EAC is absent (A,...

Fig 10: Congenital right incudomalleolar luxation (A). The incus is located anteriorly...

Fig 11: Malrotation of the malleus head and incus body (A, thick arrow) and Lateral SCC...

Fig 12: Increased mastoid and temporal bone pneumatization.

Fig 13: Subtypes of cochlear hypoplasia.

Fig 14: Subtypes of incomplete partitions.

Fig 15: Left incomplete partition type I. There is a cystic appearance of the cochlea...

Fig 16: Right incomplete partition type II. An enlarged vestibular aqueduct and a...

Fig 17: Bilateral incomplete partition type III. There is an absence of the modiolus...

Fig 18: Complete bilateral aplasia of the SCC (arrows). There is also a soft tissue...

Fig 19: Bilateral lateral SCC dysplasia. Broad and short lateral SCC with confluent...

Fig 20: Right IAC stenosis (thin arrow) with right lateral SCC dysplasia (thick arrow)....

Fig 21: Bilateral enlarged vestibular aqueduct (arrows).