Learning objectives
To review and demonstrate imaging features and role of interventional treatment of systemic vasculitis
Background
Vasculitis is relatively rare but can involve all visceral vasculature in whole body, which cause various symptoms depending on the size of the involved vessels and the target organs. Nonspecific symptoms such as fever or general fatigue can be the cause of delay of the correct diagnosis. Intestinal hemorrhage or peritoneal/retroperitoneal hemorrhage occurs with aneurysm formation and ulceration secondary to vasculitis, which can be managed by adequate interventional techniques. Percutaneous balloon angioplasty is one of the effective treatments of renovascular hypertension due to Takayasu’s arteritis....
Imaging findings OR Procedure details
Table of content and key findings1. Polyarteritis Nodosa Aneurysms or occlusions of the visceral arteries (especially renalartery)2. Microscopic Polyangiitis MPO-ANCA, Necrotizing glomerulonephritis3. Henoch–Schönlein purpura (anaphylactoid purpura) Deposition of IgA antibody, Purpura4. Takayasu arteritis Granulomatous inflammation affecting the aorta and its major branches, pulseless disease5. IgG4-related periaortitis Idiopathic sclerosing lesion, Elevated serum IgG4 concentration6. Collagen diseases (Behçet disease) Vascular Behçet (vasculitis of the vasa vasorum of the large arteries) 1. Polyarteritis NodosaDefinition Polyarteritis nodosa (PAN) is a representative disease of abdominal vasculitis. Pathologically it is a...
Conclusion
The comprehensive knowledge of imaging findings and interventional treatment of systemic vasculitis is important for the early diagnosis and treatment of the diseases, and can contribute for good outcome.
Personal Information
Yoshiko Sagara M.D.Department of Radiology, Oita University, Faculty of Medicine1-1 Idaigaoka Hasama-machi, Oita, JapanEmail:
[email protected]:+81-97-586-5934 fax:+81-97-586-0025
References
Jennette JC, Falk RJ, Andrassy K, et al. Nomenclature of systemic vasculitides. Proposal of an international consensus conference. Arthritis Rheum 1994;37:187-192 Jennette JC, Falk RJ. Clinical and pathological classification of ANCA-associated vasculitis: what are the controversies? Clin Exp Immunol 1995;101 Suppl 1:18-22 Kussmaul A, Maier R. Uber eine bisher nicht beschreibene eigenthumliche Arterienerkrankung [Periarteriitis nodosa], die mit Morbus Brightii und rapid fortschreitender allgemeiner Muskellaihmung einhergeht. Dtsch Arch Klin Med 1866; 1:484-518.Provenzale JM, Allen NB. Neuroradiologic findings in polyarteritis nodosa. AJNR Am J Neuroradiol 1996;17:1119-1126Ha HK,...