Abernethy malformations are rare congenital portomesenteric-systemic shunts bypassing the liver [1]. In 1973, John Abernethy first described this condition in the post mortem examination of a 10 year old girl [1,2]. In this poster, we are describing contrast enhanced CTimaging findings in three patients with Abernethy malformations we came across in our hospital in Hyderabad, India with aprimary goal to familiarize radiologistswith Abernethy malformations and its classification.

Abernethy malformations also known as Congenital Extrahepatic Portosystemic Shunts (CEPS) areassociated with complete or partial diversion of portal blood into systemic veins {inferior vena cava(IVC), iliac veins or renal veins} through extrahepatic shunts [1,2]. A. CLINICAL PRESENTATION: Abernethy malformations manifest with a variety of clinical symptoms [3]. CEPScan be an incidental finding or present with jaundice, abdominal mass, shortness of breath, cyanosis, clubbing, liver failure and can even cause hepatic encephalopathy [1,3]. It isseen in association with congenital heart diseases, nodular liver lesions, hepatocellular carcinoma,...

CASE1: A 10 year old boy presented with shortness of breath. He was suspected to have Abernethy malformation on echocardiography and was referred for CECT (Contrast Enhanced CT) abdomen. CECT abdomen ( Fig. 2 ) images showedsplenic vein (SV) and superior mesenteric vein (SMV) joining to form a small extra-hepatic portal vein (PV). Distal portion of extrahepatic PV wasdilated and bulbous before joining the inferior vena cava (IVC). Right and left intrahepatic portal vein branches werenot visualised. Imaging features were suggestiveof type 1b Abernethy malformation....

Abernethy malformations are diagnosed radiologically and its management is dependent on patient factors andtype of malformation [6]. Hence, radiological familiarity with this rare congenital condition will helpin making an early diagnosis and initiate prompttreatment [6].

[1]Eduardo Alonso-Gamarra, Manuel Parrón, Ana Pérez,Consuelo Prieto, Loreto Hierro, Manuel López-Santamaría (2011)Clinical and Radiologic Manifestations of Congenital Extrahepatic Portosystemic Shunts: A Comprehensive Review. Radiographics;31:707–722. [2]Atin Kumar, Jyoti Kumar, Rakesh Aggarwal, Siddharth Srivastava (2008)Abernethy malformation with portal veinaneurysm.Diagn Interv Radiol; 14:143-146. [3]Samarjit S Ghuman, Saumya Gupta, T B S Buxi et al. (2016)The Abernethy malformation—myriad imaging manifestations of a single entity. Indian J RadiolImaging. Jul-Sep; 26(3): 364–372. [4] Morgan G, Superina R. (1994) Congenital absence of the portal vein: two cases and a proposed classification system...