Learning objectives
1. To describe the role of various imaging modalities used in the investigation of primary abdominal teratomas of infancy.
2. To highlight the importance of establishing anatomical boundaries and in particular the vascular anatomy in relation to these tumours for pre-operative planning.
Background
Abdominal germ cell tumours in infancy are extremely rare, accounting for 5% of paediatric tumours. They present most commonly as an enlarging abdominal mass in the first few months of life. The imaging features are typical of teratomas with fat and calcific components. The considerable size of these tumours often leads to marked displacement of adjacent structures and in particular the major abdominal vessels. The exact site of origin can often be difficult to ascertain.Importantly, complete resection of the tumour can be challenging due to...
Findings and procedure details
We present our single institution experience in the imaging of infantile retroperitoneal teratomas over the period between 2009-2019 during which time we encountered 11 suchcases. All patients were investigated initiallywith US followed by cross-sectional imaging in the form of MR and/or CT to assess the anatomy.
The age of presentation ranged from birth to 10 months of age in our cohort. 7 patients were female and 4 were males. Patients presented with a rapidlyenlarging abdominal mass and the first line imaging modality performed was ultrasound....
Conclusion
Primary abdominal teratomas in infants have typical imaging characteristics of teratomas. Surgical resection can be hazardous due to tumour extent, unusual vascular encasement and displacement of adjacent structures. Cross section imaging in the form of T2 SPACE MRI and contrast enhanced CT can be particularly helpful in delineating the distorted vascular anatomy.
Personal information and conflict of interest
F. Sheikh; London/UK - nothing to disclose K. McHugh; London/UK - nothing to disclose
References
Operative considerations in pediatric retroperitoneal teratomas--a review.Jones VS1, Burns CR.
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Primary retroperitoneal teratomas: a review of the literature.Gatcombe HG1, Assikis V, Kooby D, Johnstone PA.
Curr Opin Pediatr. 2009 Jun;21(3):344-9. doi: 10.1097/MOP.0b013e32832b41ee.Teratomas in infants and children.
Upper abdominal teratomas in infants: radiological findings and importance of the vascular anatomy.Hart J1, Mazrani W, Jones N, Kiely EM, Sebire NJ, McHugh...