to review the following points that are essential for high quality healthcare in lifelong follow-up of patients with congenitally corrected transposition of great arteries (ccTGA); Anatomy, physiology and clinical picture of ccTGA Available options for surgical treatment and the anatomy of the postoperative heart Potential complications of ccTGA Cardiac imaging methods used in patient follow-up

Anatomy and physiology ccTGA is a rare acyanotic congenital heart defect that occurs in less than 0,5% of all congenital heart disease [1,2], also known as levo-transposition of the great arteries. It is characterized by “double discordance” of atrio-ventricular and ventriculo-arterial connections Fig. 1,and often accompanied by other cardiovascular malformations - more than 90% of patients have associated anomalies like ventricular septal defect (VSD) Fig. 4 , left ventricular outflow tract (LVOT) obstruction and valve anomalies [3]. The discordant connections at both the atrioventricular and...

The natural history of ccTGA aside from the coexisting abnormalities is mainly dictated by the systemic RV function, so the regular assessment of ventricular function is vital. In addition to routine echocardiography examination, cardiac magnetic resonance imaging (MRI) is considered to be the method of choice for a comprehensive evaluation of both asymptomatic patients and those after surgery. Compared to echocardiography, the major advantage of MRI is the ability to assess cardiac anatomy in multiple planes with high spatial resolution. Since the main feature of...

Cardiac MRI represents an ideal tool for noninvasive follow-up in all patients with RV dysfunction. It allows early recognition of ventricular dilation and impending failure, which helps the either medical or surgical treatment of ccTGA. Defining the group of ccTGA patients who remain asymptomatic and may never require surgery is of paramount importance because late diagnosis and inadequate evaluation of progressive RV dysfunction greatly impact the quality of life. Today there is still a significant number of patients treated by physiological surgery, while the anatomical...

Tihana Balaško Josipović, MD,Department of Radiology, UHC Zagreb, Croatia (UHCZ), [email protected]; Miroslav Muršić, MD, UHCZ,[email protected]; Ivica Sjekavica, UHCZ, [email protected]; Maja Hrabak Paar, MD, PHD, UHCZ, [email protected]. The authors have nothing to disclose.

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