Type:
Educational Exhibit
Keywords:
Anatomy, Cardiovascular system, Emergency, Catheter arteriography, CT, CT-Angiography, Biopsy, Chemoembolisation, Drainage, Dissection, Infection, Inflammation
Authors:
Z. Moudafia, B. dahmani, S. Omari Tadlaoui, S. Rachidi Alaoui
DOI:
10.26044/ecr2022/C-19009
Background
Systemic scleroderma (SSc) is a multisystem connective tissue disease characterized by small-vessel abnormalities , organ fibrosis and autoantibody production.
Fibrosis can affect the integumentary, musculo- skeletal, pulmonary, cardiac, gastrointestinal (GI), and urinary systems . (1)
The skin is the most involved organ in SSc and its main expression is severe Raynaud's phenomenon (RP) (2).
Cardio-pulmonary complications make the severity of scleroderma: Pulmonary arterial hypertension, heart failure, and infiltrative lung disease (ILD).(3,4)
Its diagnosis is based on clinical examination , paraclinical examinations can identify visceral complications
Conventional radiography, chest CT, echocardiography, enterography, and panorex dental imaging are commonly performed in SSc patients. (5)
Applications of ultrasonography and MRI for musculoskeletal and cardiac evaluation in systemic sclerosis are evolving.(5)