Clinical and radiological features of congenital and acquired urachal remnant diseases

This poster is published under an open license. Please read the disclaimer for further details.

Congress:

ECR 2015

Poster Number:

C-2538

Type:

Educational Exhibit

Keywords:

Urinary Tract / Bladder, CT, Ultrasound, Diagnostic procedure, Education and training

Authors:

V. S. Teran Pareja, A. Martínez Arnaiz, N. Guerrero Salcedo, E. Prado Miranda, E. Rico Aragón, E. Martínez Carapeto; Madrid/ES

DOI:

10.1594/ecr2015/C-2538

DOI-Link:

https://dx.doi.org/10.1594/ecr2015/C-2538

Fig. 3: ANATOMY OF THE URACHUS. Lower anterior abdominal wall from inside the...

Fig. 2: EMBRYOLOGY OF THE URACHUS. The cranioventral end of the bladder opens into the...

Fig. 4: TYPES OF URACHAL ANOMALIES. A. Normal obliteration of the urachal lumen. B....

Fig. 5: PATENT URACHUS. Fig. A-B-C show a 2 months-old infant with urine leakage out...

Fig. 10: URACHAL ADENOCARCINOMA. 36-year-old man with hematuria. A mass of solid...

Learning objectives

To review the anatomy and embryology of the urachus and to describe and illustrate the clinical and radiological features of the different abnormalities in both congenital and acquired urachal remnant diseases.

Background

The urachus, also known as median umbilical ligament, is a remnant of the development of two embryonic structures: the cloaca, which is the cephalic extension of the urogenital sinus, and the allantois, which is a derivative of the yolk sac. Fig. 1 Between the fourth and seventh week of life, the cloaca becomes divided into two embryological structures: the anorectal canal posteriorly and the primitive urogenital sinus anteriorly. The cephalic extension of the urogenital sinus will be the precursor of the fetal bladder, which is...

Findings and procedure details

CONGENITAL URACHAL ANOMALIES Congenital anomalies of the urachus are twice as common in menthan in women. There are five types of congenital anomalies: patent urachus, umbilical-urachal sinus, vesicourachal diverticulum, urachal cyst and alternating sinus. The patent urachus is purely congenital and represents about 50% of all cases of congenital anomalies. The others arenormallyclosed atbirth, but become reopened in association with pathological conditions that are often classified as acquired diseases. These anomalies are usually associated with congenital abnormalities of the lower urinary tract such as posterior...

Conclusion

Because the urachal remnant diseases are rare and have nonspecific clinical or imaging features, presurgical diagnosis is not easy. Knowing the basic anatomy and embryology of the urachus and its radiological characteristics is essential for the correct diagnosis of congenital and acquired anomalies

Personal information

References

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