Learning objectives
To illustrate the epidemiology, signs and symptoms of benign and malignant coronary artery anomalies (CAA)
To review the role of the different imaging methods, including cardiac ultrasound, invasive coronary angiography, computed tomography angiography, magnetic resonance angiography and myocardial perfusion single-photon emission tomography in the diagnosis and management of affected patients, understanding when surgical treatment in indicated.
Background
CAA are the variants of origin, number and the relative different course compared to the normal condition. CAA represent the second cause of sudden cardiac death (SCD) (12-19%) under the age of 35, after hypertrophic cardiomyopathy (36%). SCD usually occurs during or immediately after intense exercise. In most cases (55%), CAA are clinically silent and are recognized only at the time of autopsy with less than 10% of subjects receiving a correct pre-mortem cardiological evaluation [1].
Findings and procedure details
The prevalence of CAA is not high (1-2%), but early diagnosis and adequate clinical management are important, therefore it is necessary to rule out CAA inyoung athletes with symptoms (such as syncope, chest pain, arrhythmia). It is useful in this group of patients to find a "non-invasive" screening tool that replaces traditional coronary angiography.
There are different systematic classifications of CAA based on their anatomical features as indicated by Kim. et al., modified from Greenberg classification: [Table 1] anomalies of origin, course and termination.
CAA...
Conclusion
Non-invasive techniques are nowadays the standard for an accurate diagnosis of CAA, with very low or no radiation exposure
The radiological findings help the adequate work-up of the affected patients in order of preventing SCD.
Personal information and conflict of interest
A. Ciuni; Parma/IT - nothing to disclose A. Palumbo; Parma/IT - nothing to disclose N. Sverzellati; Parma/IT - nothing to disclose
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