Type:
Educational Exhibit
Keywords:
Cardiac, Contrast agents, MR, Education, Tissue characterisation, Retrospective, Observational, Performed at one institution
Authors:
S. Pradella1, M. Letteriello1, C. De Amicis1, M. Acquafresca1, E. Bertelli1, G. Grazzini1, V. Miele2; 1Florence/IT, 2FIRENZE/IT
DOI:
10.26044/ecr2020/C-13948
Background
The cardiac tumor is extremely rare in children, but fibromas are the second most common type of pediatric cardiac tumor, after rhabdomyoma, and the most cardiac resected neoplasms in the pediatric population [1-3].
Cardiac fibromas are mainly composed of connective tissue and fibroblast. Although benign, they can be symptomatic due to inflow and outflow tract obstruction, intracavitary obstruction, coronary artery impairment, thromboembolic events, conduction defects, and can also lead to sudden death [4]. Their clinical presentation depends upon their location and size.
Echocardiography and MR imaging are the most commonly used imaging modalities for the evaluation of cardiac masses in children [5] (Fig.1).
Fig. 1: Three young patients with ECG alterations; at echocardiography the cardiac fibromas are generally well circumscribed and echogenic; however, in some cases, their appearance may mimic that of hypertrophic cardiomyopathy, especially if they are located in the septum. CMR adds more information about the characteristics of the lesion.
Fig. 1